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We report the case of an asymptomatic unilateral pigmented paravenous retinochoroidal atrophy (PPRCA) in a 43-year-old patient. The right eye showed chorioretinal atrophy with bone-spicule-like pigmentations along the retinal veins. Visual acuity was 20 / 20 and perimetry revealed scotomas correlating to the chorioretinal atrophy. Electrophysiological examination showed decreased signals in ERG and EOG. Fundus autofluorescence and angiography findings are presented. Pathogenetically, a classification as hereditary retinal dystrophy (as in retinitis pigmentosa) as well as a post-inflammatory residuum are discussed.

Original publication




Journal article


Klin Monbl Augenheilkd

Publication Date





791 - 793


Adult, Atrophy, Choroid, Cicatrix, Electroretinography, Female, Fluorescein Angiography, Fundus Oculi, Humans, Hyperpigmentation, Retina, Retinal Vein, Retinal Vein Occlusion, Visual Fields