A novel human iPSC model of COL4A1/A2 small vessel disease unveils a key pathogenic role of matrix metalloproteinases in extracellular matrix abnormalities
Al-Thani M., Goodwin-Trotman M., Bell S., Patel K., Fleming LK., Vilain C., Abramowicz M., Allan SM., Wang T., Cader Z., Horsburgh K., Van Agtmael T., Sinha S., Markus HS., Granata A.