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The incidence, mode of presentation and management of Dancing Eye Syndrome/Opsoclonus-Myoclonus Syndrome (DES/OMS) was prospectively evaluated in 20 United Kingdom (UK) paediatric neurology centres by questionnaire over a 24-month period between 2003 and 2005. Nineteen children were notified, giving an incidence of 0.18 cases per million total population per year. Mean age at presentation was 18 months (range 3-42 months). Fifteen families consented to participate in the study. Atypical features were present in 6/15 cases including very delayed presentation of opsoclonus, dysphagia, and rapid spontaneous improvement without treatment. Only 4/15 cases were associated with neuroblastoma (NB) but current practice in excluding this is diverse and a standardised approach is suggested.

Original publication

DOI

10.1016/j.ejpn.2009.03.002

Type

Journal article

Journal

Eur J Paediatr Neurol

Publication Date

03/2010

Volume

14

Pages

156 - 161

Keywords

Abdominal Neoplasms, Brain Neoplasms, Catecholamines, Child, Preschool, Deglutition Disorders, Female, Humans, Incidence, Infant, Magnetic Resonance Imaging, Male, Neuroblastoma, Opsoclonus-Myoclonus Syndrome, Prevalence, Prospective Studies, Remission, Spontaneous