Cookies on this website
We use cookies to ensure that we give you the best experience on our website. If you click 'Continue' we'll assume that you are happy to receive all cookies and you won't see this message again. Click 'Find out more' for information on how to change your cookie settings.

OBJECTIVE: We report what we believe to be a unique aetiology of the superior semicircular canal dehiscence syndrome, a recently described condition in which vestibular imbalance and/or hearing loss results from the loss of continuity of the bone overlying the superior semicircular canals. CASE REPORT: A 58-year-old woman presented with autophony in the right ear and momentary imbalance when shouting (Tullio phenomenon). Temporal bone computed tomography revealed a defect of the right superior semicircular canal caused by an enlarged superior petrosal sinus receiving drainage from a large cerebellar developmental venous anomaly. CONCLUSIONS: We review superior semicircular canal dehiscence syndrome and its management, and we discuss common aetiologies, contrasting these with the unusual aetiology presented here. We conclude that superior semicircular canal dehiscence syndrome may present with a solely developmental aetiology, despite presenting late in life.

Original publication

DOI

10.1017/S0022215108001965

Type

Journal article

Journal

J Laryngol Otol

Publication Date

07/2008

Volume

122

Pages

741 - 744

Keywords

Audiometry, Pure-Tone, Ear, Middle, Female, Hearing Loss, Sensorineural, Humans, Meniere Disease, Middle Aged, Radiography, Semicircular Canals, Syndrome, Temporal Bone, Treatment Outcome, Vestibular Diseases